Pulmonary Fibrosis Patient

Understanding Cystic Fibrosis and Its Causes

Fibrosis

Cystic fibrosis is a chronic condition wherein it affects various organs such as the liver, lungs, pancreas, and intestines.

Patients with chronic cystic fibrosis have disrupted salt levels in the body. There are little salts and water levels in the outside of the cells of the body which causes the thin layer of mucus that protects the lungs to become sticky and thick.

The mucus becomes difficult to cough out and clogs the airways which leads to infection and damaged lungs. This disease is considered to be a hereditary disease which leads to multiple organ failure as the condition worsens. The mucus caused by CF also affects digestion through the obstruction of pancreas and inhibiting natural enzymes from helping the body to break down and absorb the nutrients from the food eaten.

Since CF is a hereditary condition, it is mainly caused by a mutation in the genes. A certain gene called cystic fibrosis transmembrane conductance regulator works for an important function in the body. This gene is involved in creating sweat, mucus, and digestive juices. You only need one copy of this gene so that you can prevent the occurrence of CF, although most people have two copies. If a person lacks at least one unaltered version of this gene, it can result to CF.

Depending on the type of mutation that the gene has, the severity of CF is variable. Actually, there are almost 1,400 different mutations of the mentioned gene. However, the most common symptoms associated with this condition include wheezing, shortness of breath, little weight gain even with good appetite, poor growth, nasal polyps, skin that tastes very salty, persistent coughing often accompanied with phlegm or extra mucus, and greasy or bulky stools.

A genetic test is done in order to diagnose the presence of CF. Aside from that, there are also several other tests that can be ordered by the physician such as X-rays, CT scans, lung function tests, sputum examinations and blood tests.

In general, there is no cure for CF. Treatment is directed towards improving the quality of life of the patients with the condition. The main goal is to clear the airways and replace enzymes so that nutrients will be properly absorbed.

No matter what sickness or condition you may have, it is always important to keep your body healthy and engage in physical activities. You can contact personal trainer Sydney to get more information about trainings and workouts that are suitable for you.